Journal of South Asian Federation of Obstetrics and Gynaecology

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VOLUME 16 , ISSUE 2 ( March-April, 2024 ) > List of Articles

Original Article

Pregnancy Outcome in Eisenmenger Syndrome at an Indian Tertiary Center

Divya Pandey, Jyotsna Suri, Rekha Bharti

Keywords : Cyanotic heart disease in pregnancy, Pulmonary hypertension in pregnancy

Citation Information : Pandey D, Suri J, Bharti R. Pregnancy Outcome in Eisenmenger Syndrome at an Indian Tertiary Center. J South Asian Feder Obs Gynae 2024; 16 (2):68-73.

DOI: 10.5005/jp-journals-10006-2061

License: CC BY-NC 4.0

Published Online: 23-02-2024

Copyright Statement:  Copyright © 2024; The Author(s).


Abstract

Aim: To evaluate the materno-fetal outcome of pregnancy with Eisenmenger syndrome (ES). Materials and methods: This retrospective observational study was carried out at a tertiary teaching institute over a 1-year period. The occurrence of ES in pregnant women with the cardiac disease along with their materno-fetal outcomes was analyzed. Results: Among 27,259 antenatal women who delivered over a period of 1 year, 104 had cardiac disease with 31 congenital heart disease (CHD). Only three cases of pregnancies with ES were found among 104. Thus, ES was seen in 1:9086 pregnant women, 1:35 pregnant women with cardiac disorders, and 1:10 pregnant women with CHD. The mean age was 25.3 ± 0.58 years while the mean gestational age (GA) at delivery was 35.23 ± 0.67 weeks. The mean pulmonary arterial pressure was 68.7 ± 13.3 mm Hg. All had preterm deliveries. Vaginal delivery was conducted in 66.7% while 33.3% had a cesarean delivery. No maternal mortality was seen. Fetal demise was seen in one of three cases. Conclusion: Multidisciplinary care with the availability of a critical care unit can help achieve a positive materno-fetal outcome in ES during pregnancy which till now has been known to have a very high mortality rate. Clinical significance: Of all CHD in pregnancy, ES is associated with a very high maternal mortality rate. However, with multidisciplinary effort and approach, optimum outcomes are achievable.


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