Journal of South Asian Federation of Obstetrics and Gynaecology

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VOLUME 10 , ISSUE 4 ( October-December, 2018 ) > List of Articles


An Unusual Case of Vulvovaginal Mass: Aggressive Angiomyxoma

Sunesh Kumar, Neeta Singh, Richa Vatsa, Jyoti Meena, Aishwarya Parthsarthy

Keywords : Aggressive angiomyxoma, Recurrence, Vulvovaginal mass

Citation Information : Kumar S, Singh N, Vatsa R, Meena J, Parthsarthy A. An Unusual Case of Vulvovaginal Mass: Aggressive Angiomyxoma. J South Asian Feder Obs Gynae 2018; 10 (4):270-272.

DOI: 10.5005/jp-journals-10006-1604

License: CC BY-NC 4.0

Published Online: 01-10-2018

Copyright Statement:  Copyright © 2018; The Author(s).


Aim: To sensitize clinician about aggressive angiomyxoma as an unusual cause of vulvovaginal mass. Background: Aggressive angiomyxoma (AA) is not a well known entity. Preoperative diagnosis is often incorrect, and most of the cases are detected on histopathological examination. Case description: A 45-year-old female, presented with the complaint of slow-growing mass in perineal area for 2 years. A large irregular firm to cystic mass, arising from the posterior wall of the vagina and protruding out of introitus extending into right ischiorectal fossa. Contrast enhanced computed tomography (CECT) revealed a well-defined mass in right perineum arising from the right lateral vaginal wall with ischiorectal fossa extension. Wide local excision was done under general anesthesia. Histopathology showed AA. Conclusion: Aggressive angiomyxoma (AA) is often misdiagnosed due to the rarity of this entity and absence of diagnostic features, but it should be considered in case of masses in the perianal region in reproductive age females. Complete surgical excision is the first line of management. Long-term follow-up is necessary. Clinical significance: Correct diagnosis of aggressive angiomyxoma is important as these tumors are benign and does not need radical surgery but recurrence is common, so long-term follow up of the patient is required. So, we reported this case to sensitize clinician about this unusual entity.

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