Journal of South Asian Federation of Obstetrics and Gynaecology

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VOLUME 9 , ISSUE 3 ( July-September, 2017 ) > List of Articles

ORIGINAL ARTICLE

Müllerian Anomalies: A Cause for Primary Amenorrhea

Anuja V Bhalerao

Citation Information : Bhalerao AV. Müllerian Anomalies: A Cause for Primary Amenorrhea. J South Asian Feder Obs Gynae 2017; 9 (3):221-224.

DOI: 10.5005/jp-journals-10006-1499

License: CC BY 3.0

Published Online: 01-12-2012

Copyright Statement:  Copyright © 2017; The Author(s).


Abstract

Introduction

Primary amenorrhea is a challenging entity as it affects the reproductive outcome. Primary amenorrhea is an absence of secondary sexual characters until 14 years of age or absence of menstruation with secondary sexual characters until 16 years of age.

Aim

The aim of this article is to study the frequency, etiologic causes, presentation, diagnosis, and optimal mode of management of primary amenorrhea.

Materials and methods

All girls who had not attained menarche until 16 years of age in the absence of secondary sexual characters and until 14 years, if no secondary sexual characters, and were willing for follow-up were subjected to investigations and were treated as per the etiology.

Results

Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome was the most common cause of primary amenorrhea (42.85%) followed by imperforate hymen (28.57%) and transverse vaginal septum (21.42%), one each of low, mid, and high varieties. There was one case of androgen insensitivity syndrome.

Conclusion

Establishing correct diagnosis is essential for planning treatment and management strategies in primary amenorrhea as treatment goals are preservation of fertility and progression of normal development.

How to cite this article

Bhalerao AV, Garg R. Müllerian Anomalies: A Cause for Primary Amenorrhea. J South Asian Feder Obst Gynae 2017;9(3):221-224.


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